Table IVa-c.

Intercorrelations among similar Unified Batten Disease Rating Scale (UBDRS) and Child Behaviour Checklist (CBCL) higher-order scales

(a) Frequency of mood, aggression, and total problems (Spearman’s rho)
	UBDRS mood	UBDRS aggression	UBDRS total problems
UBDRS physical subscale	0.14	−0.23	0.01
CBCL internalizing problems	0.41^a	0.46^b	0.53^b
CBCL externalizing problems	0.31	0.72^b	0.64^b
CBCL total problems	0.39^a	0.65^b	0.72^b

(b) Severity of mood, aggression, and total problems (Spearman’s rho)
	UBDRS mood	UBDRS aggression	UBDRS total problems
UBDRS physical subscale	0.11	−0.24	0.05
CBCL internalizing problems	0.41^a	0.46^b	0.47^b
CBCL externalizing problems	0.30	0.73^b	0.59^b
CBCL total problems	0.36^a	0.65^b	0.64^b

(c) Product of frequency and severity ratings for mood, aggression, and total problems (Spearman’s rho)
	UBDRS mood	UBDRS aggression	UBDRS total problems
UBDRS physical subscale	0.11	−0.24	0.01
CBCL internalizing problems	0.41^a	0.47^b	0.52^b
CBCL externalizing problems	0.34^a	0.72^b	0.54^b
CBCL total problems	0.39^a	0.65^b	0.58^b

p<0.05

p<0.01.

UBDRS mood: UBDRS sad + apathy + anxiety. UBDRS total aggression: UBDRS aggression to self + aggression to others. UBDRS total: UBDRS total behaviour problems (UBDRS mood + UBDRS aggression + UBDRS hallucinations + UBDRS obsessions + UBDRS repetitive behaviours).