Table 1.
Preoperative Phenotype and A1A Enzyme Activity of 39 Liver Transplant Recipients
| Children |
Adults |
||||||
|---|---|---|---|---|---|---|---|
| No. of | Serum A1A mg/dL* |
Serum A1A mg/dL* |
|||||
| Patients | Phenotype | Mean | Range | Patients | Phenotype | Mean | Range |
| 22 (76%) | PiZZ | 43.3 | (0.4–80) | 8 (80%) | PiZZ | 28.3 | (12–45) |
| 2 (7%) | PiSZ | 121.5 | (38.2–285) | ||||
| 2 (7%) | PiMZ | 121.5 | (38.2–285) | 2 (20%) | PiMZ | 90.0 | (70–115) |
| 3 (10%) | Unknown | Unknown | |||||
| n = 29 | n = 10 | ||||||
Normal = 85.0 to 213 mg/dL.