Table 1.
Reference | No. of cases | Initial presentation (PF, pulmonary fibrosis; V, vasculitis; S, simultaneous) | Positive anti-MPO preceding vasculitis (where PF occurred first) |
---|---|---|---|
[7] | 2 | PF, 2 | Unknown |
[2] | 27 | Unknown | |
[8] | 3 | Unknown | |
[9] | 1 | PF | Unknown |
[10] | 1 | S | |
[11] | 4 | PF, 4 | Unknown |
[12] | 1 | PF | Unknown |
[13] | 1 | PF | Unknown |
[14] | 6 | PF, 2; S, 4 | Unknown |
[15] | 2 | S | |
[16] | 1 | PF | Yes |
[17] | 8 | Unknown | |
[18] | 19 | S, 19 | |
[19] | 15 | Unknown | |
[4] | 1 | PF | Unknown |
[20] | 1 | PF | Unknown |
[21] | 1 | S | |
[3] | 5 | PF, 4; S, 1 | Yes, 2; unknown, 2 |
[22] | 1 | PF | Unknown |
[23] | 12 | PF, 3; V, 1; S, 8 | Unknown |
This case | 1 | PF | No |