Table 1.

Summary of cases in the literature of PF in association with anti-MPO positive vasculitis

Reference	No. of cases	Initial presentation (PF, pulmonary fibrosis; V, vasculitis; S, simultaneous)	Positive anti-MPO preceding vasculitis (where PF occurred first)
[7]	2	PF, 2	Unknown
[2]	27	Unknown
[8]	3	Unknown
[9]	1	PF	Unknown
[10]	1	S
[11]	4	PF, 4	Unknown
[12]	1	PF	Unknown
[13]	1	PF	Unknown
[14]	6	PF, 2; S, 4	Unknown
[15]	2	S
[16]	1	PF	Yes
[17]	8	Unknown
[18]	19	S, 19
[19]	15	Unknown
[4]	1	PF	Unknown
[20]	1	PF	Unknown
[21]	1	S
[3]	5	PF, 4; S, 1	Yes, 2; unknown, 2
[22]	1	PF	Unknown
[23]	12	PF, 3; V, 1; S, 8	Unknown
This case	1	PF	No