Table 1.
Families With KS With 2 Affected Siblings
| Family No. | Case No.* | Age at Onset, y | Interval, y† | Ethnicity | No. of Criteria for KS Met‡ | Medical Records Reviewed | Parental Interview Conducted | No. of IVIG Doses | Aneurysms |
|---|---|---|---|---|---|---|---|---|---|
| 1 | 1 | 1 | 1.83 | Filipino/Korean | 4 | Yes | No | 1 | No |
| 2 | 0.33 | 4 | Yes | No | 1 | No | |||
| 2 | 1 | 5 | 1.42 | Korean | 5 | Yes | No | 1 | No |
| 2 | 3 | 5 | Yes | No | 1 | No | |||
| 3 | 1 | 4 | 2.50 | Japanese | 5 | Yes | No | 1 | No |
| 2 | 6 | 5 | Yes | No | 1 | No | |||
| 4 | 1 | 3 | 0.66 | White | 4 | No | Yes | 2 | Yes |
| 1§ | 3.66 | 4 | No | Yes | 1 | ||||
| 2 | 0.67 | >1 | 4 | No | Yes | 2 | No | ||
| 5 | 1 | 12 | >1 | White | 5 | Yes | Yes | 2 | No |
| 2 | 0.75 | 5 | Yes | Yes | 1 | No | |||
| 2§ | 5 | >1 | 5 | Yes | Yes | 1 | No | ||
| 6 | 1 | 6 | 0.23 | White | 4 | Yes | Yes | 2 | No |
| 2 | 4 | 4 | Yes | Yes | 1 | No | |||
| 7 | 1 | 10 | 0.06 | White | 4 | No | Yes | 1 | Yes |
| 2 | 2.50 | 4 | No | Yes | 0 | No | |||
| 8 | 1 | 4.17 | 4.67 | White | 3 | Yes | No | 0 | No |
| 2 | 1.58 | 4 | Yes | No | 1 | No | |||
| 9 | 1 | 0.46 | 0.02 | Mexican American | 5 | Yes | Yes | 1 | No |
| 2 | 0.48 | 5 | Yes | Yes | 2 | No |
Abbreviations: IVIG, intravenous immunoglobulin; KS, Kawasaki syndrome.
Numbered in the order of KS occurrence.
Time between KS episodes in the first and second child.
The total number possible was 5, including rash, conjunctival injection, changes in the oropharynx, changes in the extremities, or a cervical lymph node larger than 1.5 cm.
Recurrent case.