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. Author manuscript; available in PMC: 2010 Jul 27.
Published in final edited form as: Arch Pediatr Adolesc Med. 2005 Sep;159(9):876–881. doi: 10.1001/archpedi.159.9.876

Table 2.

Families With KS With Complex Pedigrees

Family No. Case No.* Age at Onset, y Ethnicity No. of Criteria for KS Met Medical Records Reviewed Parental Interviews Conducted No. of IVIG Doses Aneurysms Died
10 1 NA NA NA No NA NA NA No
2 0.33 Mexican American 3 Yes No 1 No No
3 2 Mexican American 4 Yes No 2 No No
11 1 4 White 4 No Yes 1 No No
2 9 White 1 Yes Yes 0 Yes Yes
3 7 White 2 No Yes 1 Yes No
4 9 White 4 No Yes 1 No No
12 1 4.50 White 3 No No 0 No No
2 2.75 Mexican American/white 4 Yes Yes 0 Yes Yes
3 2.80 Mexican American/white 4 Yes Yes 1 No No
13 1 1.67 White 3 Yes Yes 1 No No
2 10 White 3 Yes Yes 1 No No
3 13 White 4 No Yes 1 No No
14 1 10 White 5 No Yes 0 No No
2 0.83 White 5 No Yes 1 No No
15 1 20s Mixed 5 No Yes 0 No No
2 13 Mixed 5 Yes Yes 1 No No
16 1 6 White 5 Yes Yes 0 Yes Yes
2 1.50 White 5 No Yes 1 No No
17 1 3 Japanese NA NA NA 1 No No
2 0.29 Japanese/white 4 Yes Yes 1 Yes No
18 1 6 White 5 No Yes 0 NA No
2 5 White 5 No No 0 NA No
3 2 White 4 Yes Yes 1 No No

Abbreviations: IVIG, intravenous immunoglobulin; KS, Kawasaki syndrome; NA, data not available.

*

Numbered in the order of KS occurrence.

The total number possible was 5, including rash, conjunctival injection, changes in the oropharynx, changes in the extremities, or a cervical lymph node > 1.5 cm.