Table 2.
Families With KS With Complex Pedigrees
| Family No. | Case No.* | Age at Onset, y | Ethnicity | No. of Criteria for KS Met† | Medical Records Reviewed | Parental Interviews Conducted | No. of IVIG Doses | Aneurysms | Died |
|---|---|---|---|---|---|---|---|---|---|
| 10 | 1 | NA | NA | NA | No | NA | NA | NA | No |
| 2 | 0.33 | Mexican American | 3 | Yes | No | 1 | No | No | |
| 3 | 2 | Mexican American | 4 | Yes | No | 2 | No | No | |
| 11 | 1 | 4 | White | 4 | No | Yes | 1 | No | No |
| 2 | 9 | White | 1 | Yes | Yes | 0 | Yes | Yes | |
| 3 | 7 | White | 2 | No | Yes | 1 | Yes | No | |
| 4 | 9 | White | 4 | No | Yes | 1 | No | No | |
| 12 | 1 | 4.50 | White | 3 | No | No | 0 | No | No |
| 2 | 2.75 | Mexican American/white | 4 | Yes | Yes | 0 | Yes | Yes | |
| 3 | 2.80 | Mexican American/white | 4 | Yes | Yes | 1 | No | No | |
| 13 | 1 | 1.67 | White | 3 | Yes | Yes | 1 | No | No |
| 2 | 10 | White | 3 | Yes | Yes | 1 | No | No | |
| 3 | 13 | White | 4 | No | Yes | 1 | No | No | |
| 14 | 1 | 10 | White | 5 | No | Yes | 0 | No | No |
| 2 | 0.83 | White | 5 | No | Yes | 1 | No | No | |
| 15 | 1 | 20s | Mixed | 5 | No | Yes | 0 | No | No |
| 2 | 13 | Mixed | 5 | Yes | Yes | 1 | No | No | |
| 16 | 1 | 6 | White | 5 | Yes | Yes | 0 | Yes | Yes |
| 2 | 1.50 | White | 5 | No | Yes | 1 | No | No | |
| 17 | 1 | 3 | Japanese | NA | NA | NA | 1 | No | No |
| 2 | 0.29 | Japanese/white | 4 | Yes | Yes | 1 | Yes | No | |
| 18 | 1 | 6 | White | 5 | No | Yes | 0 | NA | No |
| 2 | 5 | White | 5 | No | No | 0 | NA | No | |
| 3 | 2 | White | 4 | Yes | Yes | 1 | No | No |
Abbreviations: IVIG, intravenous immunoglobulin; KS, Kawasaki syndrome; NA, data not available.
Numbered in the order of KS occurrence.
The total number possible was 5, including rash, conjunctival injection, changes in the oropharynx, changes in the extremities, or a cervical lymph node > 1.5 cm.