TABLE 1.
DIFFERENTIAL BRONCHOALVEOLAR LAVAGE COUNTS IN VARIOUS HERMANSKY-PUDLAK SYNDROME GROUPS
AMs | PMNs | Lymphocytes | |
---|---|---|---|
C57BL/6 controls | 99.5 ± 0.7 | 0 | 0.5 ± 0.7 |
HPS1/2 | 74.6 ± 5.4 | 10.7 ± 6.4 | 14.6 ± 3.5 |
HPS1 | 67 ± 40.0 | 0 | 33 ± 40.0 |
HPS2 | 93.6 ± 10.4 | 0.6 ± 0.8 | 5.8 ± 10.4 |
HPS6 | 43.8 ± 17.9 | 0.4 ± 0.2 | 55.8 ± 23 |
HPS1/6 controls | 99 ± 1.0 | 0 | 0.5 ± 0.7 |
HPS1/6 | 11.5 ± 4.8 | 0 | 88.5 ± 4.8 |
Definition of abbreviations: AMs = alveolar macrophages; HPS = Hermansky-Pudlak syndrome; PMNs = polymorphonuclear lymphocytes.
Data represent means ± SD.