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. Author manuscript; available in PMC: 2010 Oct 1.
Published in final edited form as: J Child Neurol. 2009 Jun 17;24(10):1316–1320. doi: 10.1177/0883073809333531

Table 1.

Metabolic Abnormalities During Hospitalization.

Hospital Day
1 2 3 4
Carbon Dioxide (mEq/L) 14, 19 18
AST (U/L) 38
Lactate (mMol/L) 2.4 1.9
Pyruvate (mMol/L) 0.152
Ammonia (mcg/dL) 258 441 138
Alanine (uMol) 304
Lysine (uMol) 84
Alanine/Lysine Ratio (<2.5) 3.6
Urine Organic Acids (Present) succinic, 4-OH-PHE-Acetic, aconitic, hippuric, citric, 2-oxoglutaric