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. Author manuscript; available in PMC: 2011 Aug 1.
Published in final edited form as: Pediatr Res. 2010 Aug;68(2):159–164. doi: 10.1203/PDR.0b013e3181e5c3a4

TABLE 1.

Aspartate treatment 0 mmol/kg/day 3 mmol/kg/day 6 mmol/kg/day
Methylmalonate μM 4.6 5.5 4.4
Propionylcarnitine μM 29.7 40.1 44.7
Alanine μM 549 509 568
Glutamate μM 147 288 249
Glutamine μM 678 1177 1061
Proline μM 578 553 718
Lactate mM 8.2 2.6 3.9
AST IU/L 314 265 209
ALT IU/L 185 176 123
Triglycerides mg/dL 639 223 87.5
Liver size cm BRCM 6 4 cm
Carbohydrate intake 37% of calories 47% of calories