Table 1.
Prevalence of Heart Failure and Left Ventricular Fractional Shortening Z-score at Diagnosis of Pediatric Cardiomyopathy, by Type and Cause of Cardiomyopathy. Data are from the Pediatric Cardiomyopathy Registry.
| Type of Cardiomyopathy, by Cause |
Heart Failure n |
Mean Left Ventricular Fractional Shortening Z-Score (95% CI) [Standard Deviation] |
|---|---|---|
| Dilated | ||
| Idiopathic | 74 | −9.62 (−11.42 to −7.16) |
| Myocarditis | 84 | −9.11 (−11.05 to −6.67) |
| Neuromuscular Disorders |
35 | −5.88 (−8.02 to −3.32) |
| Familial | 53 | −7.07 (−9.63 to −3.68) |
| Inborn Errors of Metabolism |
60 | −8.94 (−10.30 to −5.33) |
| Malformation Syndromes |
67 | −5.95 (−9.49 to −5.10) |
| Hypertrophic | ||
| Inborn Errors of Metabolism |
40.3 | −1.11 [5.65] |
| Malformation Syndromes |
23.4 | 5.42 [4.31] |
| Neuromuscular Disorders |
6.4 | 3.01 [3.40] |
| Infantile | 9.9 | 3.62 [5.15] |
Data from the Pediatric Cardiomyopathy Registry.