Fig. 7.

Three examples of SE T2 appearances of different orbital tumours in young children, presenting with rapidly progressive proptosis. a 4-year old boy with right sided proptosis. SE T2 image shows a high signal lesion in the medial quadrant of the orbit (arrow), presumably extraconal. Biopsy: eRMS. b 1-year old boy with rapidly progressive, left sided proptosis. SET2 shows intermediate signal intensity lesion (arrow), with central necrosis (white arrow), in the medial quadrant, compressing the lateral rectus muscle, presumably extraconal. Final diagnosis: alveolar RMS, rare at such a young age. c 2-year old girl with rapidly increasing left sided proptosis. SE T2 shows a very low signal intensity tumour in the medio-inferior part of the left orbit (arrow). Histology: primitive neuroendocrine tumour (PNET)