Table 4.
Characteristics of eleven cases of AAV in SSc.
| Characteristic | Number (%) |
|---|---|
| Sex (M/F) | 4/7 (36%/64%) |
| Age (mean ± SD) | 53 ± 14 (range from 19 to 71) |
| SSc duration (mean ± SD in yrs); 9 pts | 4.49 ± 3.37 (range from 0.42 to 10 yrs) |
| SSc Dx to AAV dx (mean ± SD in yrs); 10 pts | 3.85 ± 2.67 (range from 0.42 to 8 yrs) |
| SSc type (Diffuse/Limited) | 7/3 (64%/27%) |
| D-penicillamine use | 4 (36%) |
| Renal involvement | 9 (82%) all with crescentic GN on Bx |
| Pulmonary involvement | 2 (18%) |
| ANA + (>1 : 320) | 8 (88%) |
| Scl-70 + | 5 (45%) |
| Anticentromere + | 1 (9%) |
| MPO + | 10 (91%) |
| PR3 + | 0 |