Table 3.
Liver Diseases of Pediatric Recipients
Diseases | No. Patients |
---|---|
Biliary atresia | 179 |
Liver-based inborn metabolic errors | 63 |
(Alpha-1-antitrypsin deficiency. Wilson’s, etc) | |
Cirrhosis (postnecrotic and cryptogenic) | 39 |
Familial cholestatic syndrome | 15 |
Fulminant hepatic failure | 13 |
Secondary biliary cirrhosis | 7 |
Congenital hepatic fibrosis | 7 |
Primary hepatic malignancy | 3 |
Budd-Chiari syndrome | 2 |
Neonatal hepatitis | 2 |
Others* | 4 |
Primary sclerosing cholangitis, trauma, focal nodular hyperplasia, inflammatory pseudotumor.