Table 4.
Food and Drug Administration approved drugs for prophylaxis and treatment of hereditary angioedema attacks[18,34,35,37,38,40]
Drug | FDA approved indication | Usual adult dose | Range |
Cinryze | Prophylaxis | 1000 units IV | Every 3rd or 4th day |
Danazol | Prophylaxis | 200 mg/d | 100 mg every 3rd day to 600 mg/d |
Berinert | Acute attacks | 20 units/kg body weight IV | Per attack |
Icatibant | Acute attacks | 30 mg SQ | Per attack |
Ecallantide | Acute attacks | 30 mg SQ | Per attack |
FDA: Food and Drug Administration.