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. Author manuscript; available in PMC: 2010 Oct 26.
Published in final edited form as: Arch Surg. 1993 Mar;128(3):337–339. doi: 10.1001/archsurg.1993.01420150093017

Table 1.

Findings in 23 Patients Undergoing Liver Transplantation for Alagille’s Syndrome

Finding No. (%) of Patients
(N=23)

Intrahepatic bile duct paucity and
 cholestasis
23 (100)
Cardiovascular anomalies with
 pulmonary artery stenosis as the
 main component
23 (100)
Dysmorphic facies 15 (65)
Psychomotor retardation 14 (61)
Skeletal malformations 11 (48)
Ocular abnormalities (posterior
 embryotoxon)
10 (43.5)
Xanthomas 6 (26)