Table 1.
Findings in 23 Patients Undergoing Liver Transplantation for Alagille’s Syndrome
Finding | No. (%) of Patients (N=23) |
---|---|
Intrahepatic bile duct paucity and cholestasis |
23 (100) |
Cardiovascular anomalies with pulmonary artery stenosis as the main component |
23 (100) |
Dysmorphic facies | 15 (65) |
Psychomotor retardation | 14 (61) |
Skeletal malformations | 11 (48) |
Ocular abnormalities (posterior embryotoxon) |
10 (43.5) |
Xanthomas | 6 (26) |