Premanifest
(n=3) |
Mild
(n=15) |
Moderate
(n=6) |
Severe
(n=3) |
All HD
(n=27) |
|
Age (yrs) | 32.7 (2.5) | 49.4 (9.9) | 46.7 (14.6) | 45.0 (8.9) | 46.4 (11.3) |
Gender (F:M) | 2:1 | 2:3 | 1:1 | 0:3 | 11:16 |
Duration (yrs) | 14 (4) to onset | 5.3 (4.2) | 7.3 (3.1) | 14.0 (7.2) | 6.9 (5.1) |
CAG repeat length | 43.67 (1.16) | 43.87 (3.18) | 46.60 (5.03) | 46.67 (4.04) | 44.69 (3.59) |
Concomitant
Medication |
0 | 53% | 67% | 67% | 52% |
TFC | 13 (0) | 11.9 (0.7) | 8.0 (1.3) | 5.3 (1.2) | 10.4 (2.7) |
TMS | 0.3 (0.6) | 27 (7.8) | 55.3 (13.7) | 40.0 (13.7) | 31.8 (18.6) |
MMSE | 29.7 (.58) | 27.9 (2.2) | 25.5 (5.8) | 25.5 (5.0) | 27.3 (3.6) |
Verbal Fluency | 49.7 (21.0) | 33.2 (12.7) | 18.3 (9.2) | 20.3 (8.5) | 30.2 (15.4) |
Digit symbol | 51.0 (10.1) | 29.3 (10.1) | 22.3 (8.5) | 19.3 (2.9) | 29.0 (12.5) |
Stroop Color | 71.3 (22.7) | 49.9 (16.1) | 38.3 (11.1) | 28.0(5.7) | 47.9 (18.4) |
Stroop Word | 86.0 (15.1) | 67.7 (20.5) | 50.3 (13.3) | 35.0 (7.1) | 63.1 (21.7) |
Stroop Interference | 40.0 (14.0) | 31.4 (7.8) | 21.5 (7.0) | 17.0 (5.7) | 28.9 (10.2) |