Progressive LC3-II accumulation in NPC1 mouse
brains.
A, representative immunoblots of NPC1,
LC3-I/II, p-p70, and total p70 expression in cortical
(Ctx, panel i),
hippocampal (Hip., panel ii),
and cerebellar (Cbm., panel
iii) regions of wild type and NPC1 brains at 3 and
6 weeks and end stage (9–12 weeks). B,
histogram of LC3-II expression in NPC1 brain regions relative to
3-week NPC1 cerebellar levels (n = 5,
mean ± S.E.). Note: comparisons with corresponding wild
type mice was not possible due to undetectable basal levels of
LC3-II in healthy mice. Considering 3-week NPC1 regions had the
lowest expression of LC3-II among the NPC1 mice, their levels
were used as a base line for comparing LC3-II changes in other
NPC1 brain regions. C, histogram of
phospho-p70/total p70 expression in NPC1 brain relative to
corresponding brain regions in age-matched wild type controls
(n = 6, mean ± S.E.).