Figure 1. Strategy for targeting the expanded CAG repeat region of mutant HTT mRNA to elicit allele-selective inhibition.
(A) Schematic of the HTT mRNA and the CAG repeat region that is targeted with complementary CTG-repeat ASOs. UTR, untranslated region. (B) Chemically modified base, backbone and nucleosides incorporated into ASOs tested for allele-selective inhibition of HTT expression.