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. Author manuscript; available in PMC: 2010 Dec 1.
Published in final edited form as: Mol Genet Metab. 2010 Aug 7;101(4):324–331. doi: 10.1016/j.ymgme.2010.08.001

Fig. 6.

Fig. 6

Autophagic accumulation is noticeable on ERT. Fibers from infants were stained for LAMP-2 (red)/LC3 (green). Left: a variable response to ERT in NBS6 (A), CLIN3 (B, D), and CLIN5 (C). Right: autophagic buildup emerges upon ERT [CLIN3 (E, G, H, J) and NBS4 (F, I)]. Bar: 10 microns. (For interpretation of the references to colour in this figure legend, the reader is referred to the web version of this article.)