Table 3.

Characteristics of the three autosomal dominant cerebro-ocular vasculopathies mapped to chromosome 3.

Name	Ocular findings	Neurologic findings	Other findings
Hereditary Vascular Retinopathy (HVR)	Microangiopathy Retinal periphery and posterior pole	Multiple small lesions in GM and WM Headaches	Raynaud phenomenon
Cerebro-Retinal Vasculopathy (CRV)	Microangiopathy Posterior pole	Cerebral pseudotumors Extensive WM lesions Dementia Headaches Death <55 years
Hereditary Endotheliopathy, Retinopathy, Nephropathy and Stroke (HERNS)	Microangiopahty Posterior pole	Cerebral pseudotumors Extensive WM lesions Dementia Headaches Stroke Death <55 years	Renal involvement

WM: white matter, GM: grey matter.