Figure 4. Amounts of protein of various subunits of the respiratory chain in the patient’s muscle.

Immunoblot analysis of (A) selected subunits of respiratory complex IV (COn) and (B) representative subunits (su) of respiratory complex (RC) I, II, III and V and of VDAC and emerin, from the patient (P) and three control subjects (C1–3). See supplementary materials for antibody details and abbreviations.