Table 2.

Intergroup Rhabdomyosarcoma Study Group Staging System

Stage	Site of primary tumour	Tumour size	Lymph nodes	Distant metastases
1	Orbit, non-PM head/neck; GU nonbladder/prostate; biliary tract	Any size	N0, N1	M0
2	All other sites	<5cm	N0	M0
3	All other sites	<5cm >5cm	N1 N0 or N1	M0 M0
4	Any site	Any size	N0 or N1	M1

PM: parameningeal; GU: genitourinary; N0: no nodal involvement; N1: regional lymph node involvement; M0: no metastasis; M1: distant metastasis. Adapted from Raney et al.¹¹