Table 2.
Analysis of age at diagnosis of hereditary and sporadic PPGLs from data in eight studies
| MEN 2 |
NF 1 |
VHL |
SDHB |
SDHD |
Sporadic |
|||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Age | n | Age | n | Age | n | Age | n | Age | n | Age | n | |
| Neumann et al., 2002 (1) | 36 | 13 | n.d. | n.d. | 18 | 30 | 26 | 12 | 29 | 11 | 44 | 205 |
| Amar et al., 2005 (2) | 30 | 16 | 40 | 13 | 24 | 25 | 34 | 21 | 31 | 11 | 46 | 228 |
| Mannelli et al., 2009 (3) | 37 | 27 | 42 | 5 | 30 | 48 | 29 | 24 | 40 | 47 | 50 | 340 |
| Cascon et al., 2009 (13) | 39 | 36 | n.d. | n.d. | 28 | 20 | 30 | 25 | 25 | 11 | 46 | 143 |
| Walther et al., 1999 (14) | n.d. | n.d. | 42 | 148 | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. |
| Casanova et al., 1993 (15) | 38 | 100 | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. |
| Pomares et al., 1998 (16) | 38 | 23 | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | 47 | 23 |
| Ricketts et al., 2010 (17) | n.d. | n.d. | n.d. | n.d. | n.d. | n.d. | 27 | 153 | 21 | 18 | n.d. | n.d. |
| Grouped mean & total n | 37 | 215 | 42 | 203 | 26 | 123 | 28 | 235 | 32 | 98 | 47 | 939 |
n.d., No data presented on this group in the study.