TABLE 1.
Gene/Protein/Chromosomal Location | Mode of Inheritance | Penetrance | Age of Onset | No. Mutations/No. Families* | Availability of Clinical Testing |
---|---|---|---|---|---|
APP/amyloid precursor protein/21q21.3 | Autosomal Dominant | Complete | 40–60 | 28 in 76 families | Yes (limited) |
PSEN1/presenilin1/14q24.3 | Autosomal Dominant | Complete | 30–60 (generally before age 65) | 165 in 354 families | Yes |
PSEN2/presenilin2/1q31–42 | Autosomal Dominant | Incomplete | 40–75 | 10 in 18 families | Yes (limited) |
APOE/apolipoproteinE/19q13.32 | Complex (susceptibility) | n/a | Late onset | Not a mutation e4 polymorphism associated with increased risk | Yes (recommended for symptomatic only) |
SORL1/neuronal sortilin-related receptor/11q23 | Complex/susceptibility? | n/a | Late onset | n/a | No |
GAB2/11q14 | Complex/susceptibility? | n/a | Late onset | n/a | No |