. Author manuscript; available in PMC: 2012 May 1.

Published in final edited form as: Mitochondrion. 2011 Feb 1;11(3):488–496. doi: 10.1016/j.mito.2011.01.005

Table 1.

Respiratory chain enzyme activities from patient muscle homogenate.

Enzymes	Patient	Controls (n=31)
Complex I	0.09	0.12 – 0.28 (0.19+/− 0.04)
Complex II	0.14	0.14 – 0.36 (0.21+/− 0.05)
Complex III	0.34	0.55 – 1.11 (0.78+/− 0.15)
Complex IV	0.49	0.57 – 1.77 (1.16+/− 0.28)
Complex V	0.20	0.19 – 0.65 (0.39+/− 0.13)
Citrate synthase	112	70 – 169 (105+/− 25)

Mean value (+/− 1SD) of the activities of the respiratory chain complexes are normalized to citrate synthase (CS). Activities are expressed as mU/mg mitochondrial protein and as a percentage of the control mean. Profound deficiencies below the range of controls are shown in bold. n=number of controls.