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. Author manuscript; available in PMC: 2012 May 1.
Published in final edited form as: Am J Med Genet A. 2011 Apr 11;155(5):1202–1211. doi: 10.1002/ajmg.a.33209

Figure 1.

Figure 1

Audiograms associated with GJB2 D46N hearing loss (better hearing ear is shown). Top: Sequential audiograms from two persons in family L-1301 showing progression to severe-to-profound hearing loss. Middle: Audiograms from five persons in family L-1301 at different ages showing relatively uniform audioprofiles. Bottom: Audiograms from four persons in family L-3057 at different ages showing variably in hearing thresholds by age.