Table 2.
Clinical and laboratory data of patients at presentation
| Patient No. | 1 | 2 | 3 | 4 | 5 | 6 | 7 | 8 | 9 |
|---|---|---|---|---|---|---|---|---|---|
| Age (years) | 3 | 2 | 4 | 13 | 0.8 | 10 | 16 | 6 | 2.5 |
| Sex | F | M | M | M | M | F | F | M | F |
| Jaundice | + | + | + | - | - | + | - | - | - |
| Hepatomegaly | + | NAD | + | - | - | NAD | - | + | + |
| splenomegaly | - | NAD | + | - | - | NAD | - | - | - |
| Ascites | + | NAD | - | - | - | NAD | - | - | - |
| Total bilirubin (mg/dl) | 5.9 | NAD | 3.35 | N | N | NAD | N | N | N |
| Direct (mg/dl) | 5 | NAD | 2.6 | N | N | NAD | N | N | N |
| ALT(XN) | 2.5 | NAD | 7.2 | N | N | NAD | 1.15 | 3.4 | 2.5 |
| AST (XN) | 3.5 | NAD | 5.8 | N | N | NAD | 0.7 | 1.7 | 1.3 |
| GGT (U/L) | 128 | NAD | 183 | N | ND | NAD | 30 | 85 | 50 |
| Albumin (gm/dl) | 1.5 | NAD | 3.2 | N | N | NAD | N | N | N |
| INR | 1.7 | NAD | 1 | N | N | NAD | N | N | N |
M: male, F: female, +: present, -: absent, NAD: No available data, N: normal, ND: Not done