Table I.
Cancer in NS, CS, CFCS, and NSML literature cases
Syndrome | All cases | Cancer-free | All cancers |
---|---|---|---|
Noonan | 1151 | 1106 | 45 pts with 46 cancers (3.9%) |
Costello | 268 | 239 | 29 (10.8%) |
Cardofaciocutaneous | 226 | 218 | 8 (3.5 %) |
Noonan syndrome with multiple lentigines | 296 | 291 | 5 (1.6%) |