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. Author manuscript; available in PMC: 2012 May 15.
Published in final edited form as: Am J Med Genet C Semin Med Genet. 2011 Apr 15;157(2):83–89. doi: 10.1002/ajmg.c.30300

Table I.

Cancer in NS, CS, CFCS, and NSML literature cases

Syndrome All cases Cancer-free All cancers
Noonan 1151 1106 45 pts with 46 cancers (3.9%)
Costello 268 239 29 (10.8%)
Cardofaciocutaneous 226 218 8 (3.5 %)
Noonan syndrome with multiple lentigines 296 291 5 (1.6%)