Table 2.

Autoimmunity in the hyper-immunoglobulin M (IgM) syndromes

	CD40L [8](56 patients)	CD40L [9](79 patients)	AID [38](29 patients)
Inflammatory bowel disease	6%	–	3
Seronegative arthritis	11%	–	3
Neutropenia	44%	60
Autoimmune haemolytic anaemia	1	15	3
Immune thrombocytopenia	–	4	3
Hepatitis	–	–	3
Uveitis	–	–	3
Diabetes mellitus	–	–	3