Table 1. Characteristics of CF patients.
Patient | Age | Sex | Genotype | Microbiologya | FEV1% |
CF1 | 25 | M | F508del/- | none | 98% |
CF2 | 34 | F | F508del/F508del | S.a. | 76% |
CF3 | 16 | F | F508del/F508del | none | 87% |
CF4 | 20 | F | F508del/F508del | S.a. | 49% |
CF5 | 24 | F | F508del/R1162X | S.a,P.a. | 63% |
CF6 | 34 | F | F508del/L732X | C.a., S.a.,P.a. | 33% |
CF7 | 15 | M | F508del/F508del | A.t., S.m. | 39% |
CF8 | 22 | M | F508del/N1303K | S.a., P.a. | 39% |
CF9 | 23 | M | F508del/F508del | P.a. | 91% |
CF10 | 33 | F | F508del/F508del | P.a.,P.f. | 49% |
CF11 | 27 | F | F508del/F508del | P.a. | 28% |
CF12 | 45 | F | F508del/F508del | P.a. | 44% |
CF13 | 30 | M | W1282X/W1282X | P.a. | 43% |
CF14 | 28 | M | F508del/F508del | S.a. | 66% |
CF15 | 36 | F | F508del/F508del | S.a. | 76% |
S.a.: Staphylococcus aureus; P.a.: Pseudomonas aeruginosa; C.a.: Candida albicans; A.t.: Aspergillus terreus; S.m.: Stenotrophomonas maltophilia; P.f.: Pseudomonas fluorescens; - unknown;