Fig. 6. Western blot analysis of CI-MPR expression and GAA content of skeletal muscle following clenbuterol treatment.
(A) Western blot detection of CI-MPR and human GAA in the tibialis anterior of GAA-KO mice is shown, with molecular weights indicated. Each lane represents an individual mouse. Equivalent quantities of tissue homogenate were loaded for each mouse. (B) Signal for CI-MPR as quantified by densitometry of Western blot images. Mean +/− standard deviation are shown. Statistically significant alterations associated with CI-MPR absence indicated (*).