Table 1.
Patient Demographics and Presenting Characteristics
| Patient | Age at Onset (Years) | Gender | Race* | ILD | Raynaud’s Phenomenon | Rash | Myalgia | Arthritis | Dysphagia | Weakness on Exam** |
||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| PU | DU | PL | DL | A | ||||||||||
| 1 | 20 | F | AA | -- | + | + | + | + | + | + | + | + | − | + |
| 2 | 34 | F | AA | -- | -- | + | -- | -- | + | + | − | + | + | − |
| 3 | 42 | F | W | -- | -- | -- | -- | -- | + | + | + | + | − | − |
| 4 | 72 | M | W | -- | -- | -- | + | -- | + | + | + | + | + | + |
| 5 | 21 | F | AA | -- | + | -- | + | + | -- | + | + | + | − | + |
| 6 | 26 | F | AA | -- | + | + | -- | + | + | + | − | + | − | − |
| 7 | 51 | M | W | -- | -- | -- | + | + | + | + | − | + | − | − |
| 8 | 32 | F | W | -- | + | + | + | -- | -- | + | − | + | − | − |
Key: ILD = interstitial lung disease;
*
AA= African-American, W= Caucasian
**
PU = proximal upper extremity, DU= Distal upper extremity, PL=proximal lower extremity, DL=distal lower extremity
A= asymmetrical weakness. Weakness was defined as ≤ 4 on manual muscle strength testing