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. 2011 May 3;2011:626495. doi: 10.4061/2011/626495

Table 3.

Relationship between the results of ANCA testing and clinical diagnoses.

Diseases p-ANCA c-ANCA x-ANCA IIF (−)/ELISA (+) Anti-MPO (+) Anti-PR3 (+) Total (N)
MPA N 45 4 6 6 46 10 61
% 73.8 6.6 9.8 9.8 75.4 16.4

WG N 6 34 1 5 4 40 46
% 13.0 73.9 2.2 10.9 8.7 87

CSS N 4 0 2 0 6 0 6
% 66.7 0.0 33.3 0.0 100 0.0

CTD N 97 2 31 2 9 1 132
% 73.5 1.5 23.5 1.5 6.8 0.7

GD N 67 10 40 0 1 8 117
% 57.3 8.5 34.2 0.0 17.9 7.7

Other vasculitides N 27 1 11 0 7 3 39
% 69.2 2.6 28.2 0.0 5.6 0.0

Infections N 23 1 12 0 2 0 36
% 63.9 2.8 33.3 0.0 5.6 0.0

ND N 23 1 9 0 0 0 33
% 69.7 3.0 27.3 0.0 0.0 0.0

Malignancies N 21 1 9 0 1 0 31
% 67.7 3.3 29.0 0.0 3.3 0.0

RD N 18 0 4 0 2 0 22
% 81.8 0.0 18.2 0.0 9.0 0.0

Medication N 10 0 5 0 0 0 15
% 66.7 0.0 33.3 0.0 0.0 0.0

Miscellaneous disorders N 5 2 6 1 0 1 14
% 35.7 14.3 42.9 7.1 0.0 7.1

Undefined diagnosis N 63 4 39 3 2 3 109
% 57.8 3.7 35.8 2.7 1.8 2.7

MPA: microscopic polyangiitis, WG: Wegener's granulomatosis, CSS: Churg-Strauss syndrome, CTD: connective tissue diseases, GD: gastrointestinal diseases, ND: neurological diseases, RD: renal diseases.