Table 1.
Overall descriptives of sporadic CJD patients (n = 131)
| Characteristic | |
|---|---|
| Gender: female (%) | 77 (58.8) |
| Diagnosis classification: definite (%) | 110 (84.0) |
| Mean age at onset (years) ± SD | 65.6 ± 9.5 |
| Mean duration of disease (months) ± SD | 6.6 ± 7.0 |
| Molecular subtype | |
| MM1 (%) | 33 (53.2) |
| MM2 (%) | 4 (6.5) |
| MV1 (%) | 1 (1.6) |
| MV2 (%) | 8 (12.9) |
| VV1 (%) | 2 (3.2) |
| VV2 (%) | 14 (22.6) |
| Clinical characteristics: | |
| Typical EEG/total EEGs (%) | 50/125 (40.0) |
| Positive MRI/total MRIs (%) | 12/28 (42.9) |
| Positive CSF 14.3.3 test/total tests (%) | 46/51 (90.2) |