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. 2011 Mar 1;26(8):1215–1227. doi: 10.1007/s00467-011-1797-x

Table 1.

Important amyloid fibrils for nephrologists

Amyloid protein Precursor protein Clinical syndrome
AA Serum amyloid A protein Secondary, reactive, associated with chronic inflammatory diseases
AL Monoclonal Ig light chains Primary, associated with monoclonal plasma cell dyscrasias
AH Monoclonal Ig light chains Primary, associated with monoclonal plasma cell dyscrasias
2M β2-microglobulin Associated with dialysis
AFib Fibrinogen α-chain Familial autosomal dominant systemic amyloidosis
ACys Cystatin C Hereditary cerebral hemorrhage with cerebral and systemic amyloidosis
ALys Lysozyme Familial autosomal dominant systemic amyloidosis
AApoAI Apolipoprotein AI Familial
AApoAII Apolipoprotein AII Familial
ATTR Transthyretin Familial
AGel Gelsolin Familial