Table 1.

Clinical features of Kennedy's disease (tremor) and molecular genetic testing in 10 patients (from 7 families).

Clinical features	Patient
	1	2	3	4	5	6	7	8	9	10
Family	1	2	2	2	3	3	4	5	6	7
Age	44	21	50	41	55	50	62	50	51	45
Age at onset*	40	19	40	35	49	44	43	39	37	30
Mean number of CAG repeats	47	45	53	41	46	53	44	47	47	47
Hand postural tremor	+	+	-	-	+	+	+	+	+	+
Hand intention tremor	-	-	-	-	+	+	+	-	+	-
Head tremor	+	-	-	-	-	-	-	-	-	-
Leg tremor	-	-	-	-	+	-	-	-	-	-
Alcohol responsiveness	+	+	NT	NT	+	+	+	+	-	+
β-Blocker treatment	+	+	-	-	+	+	+	+	-	+

*Age at onset was defined retrospectively by determining the age at which the first symptom or sign attributable to Kennedy's disease was detected.

NT  =  not tested.