Table 4.

Mortality of 99 Dutch Pompe patients compared to general Dutch population

Analysis	Median follow-up time (range)	Observed no. deaths (O)	Expected no. deaths (E) *	Ratio (O/E)	P -value
1	2.3 (<1 month-7 years)	5	2.3	2.2	0.09
2	3.3 (<2 months-7 years)	9	2.8	3.2	0.002

Analysis 1: 5 deceased patients before start of ERT Analysis 2: including 4 patients who died after start of ERT with follow-up of every patient on ERT extended with 1 year after start of ERT. * According to death probabilities derived from Dutch Central Bureau of Statistics.