Table 1.

Summary of Clinical Data for Some of the Affected Individuals of Family HN-W078

Patient	Gender	Age (Years)		Use of Aminoglycoside	Hearing Test PTA∗(dB HL)		Audiogram Shape	Level of Hearing Impairment∗	Vertigo	Tinnitus
		At Testing	At Onset		Left Ear	Right Ear
II:7	female	76	24	no	80	88	flat	severe	no	yes
III:10	male	60	22	no	79	80	flat	severe	no	yes
III:13	male	59	26	no	110	76	flat	severe	no	yes
III:15	female	53	20	no	66	66	flat	moderate	no	yes
III:19	female	52	30	no	60	62	flat	moderate	no	no
IV:3	male	52	24	no	61	68	flat	moderate	no	yes
IV:6	male	49	24	no	63	64	flat	moderate	no	yes
IV:8	male	40	23	no	71	71	flat	severe	no	no
IV:10	male	55	20	no	76	78	flat	severe	no	yes
IV:24	male	30	15	no	70	70	flat	severe	no	yes
IV:26	female	26	20	no	58	55	sloping	moderate	no	yes
IV:31	male	18	12	no	48	48	flat	moderate	no	yes
IV:33	male	33	26	no	60	69	flat	moderate	no	yes
IV:35	female	31	20	no	58	59	flat	moderate	no	yes
V:13	male	27	23	no	53	54	sloping	moderate	no	no
V:27	female	23	16	no	41	44	flat	moderate	no	no

^∗The degree of hearing loss was defined according to pure-tone averages (PTAs), which were based on the frequencies 500, 1,000, and 2,000 Hz.