Table 5.
Age, yr |
||||||||||||
---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | 7 | 7 | 9 | 12 | 12 | 13 | 14 | 15 | 19 | 19 | 19 | |
Cilia defect | RS | RS | Transp | Transp | ODA | RS | ODA | Transp | RS | SODA | RS | Normal |
CBF median, Hz | 3 | 3 | 8 | 3 | 2 | 2 | 2 | 7 | 2 | 2 | 5 | 3 |
Situs inversus | + | + | − | − | + | − | + | − | + | + | − | + |
Severity of bronchiectasis (0–3) | 0 | 2 | 3 | 2 | 1 | 2 | 1 | 3 | 1 | 2 | 2 | 2 |
Peribronchial thickening (0–3) | 1 | 2 | 2 | 2 | 1 | 2 | 1 | 3 | 1 | 2 | 2 | 2 |
Extent of bronchiectasis (0–3) | 0 | 2 | 2 | 3 | 1 | 3 | 1 | 3 | 1 | 3 | 3 | 2 |
Extent of mucus plugging (0–3) | 0 | 2 | 2 | 3 | 1 | 3 | 1 | 3 | 1 | 3 | 3 | 3 |
Generations of bronchial divisions involved (0–3) | 0 | 3 | 3 | 3 | 3 | 3 | 3 | 3 | 3 | 3 | 3 | 3 |
Collapse/consolidation (0–2) | 1 | 2 | 2 | 2 | 1 | 2 | 0 | 2 | 2 | 0 | 1 | 1 |
Computed tomography scan radiological score based on the arithmetic mean of the evaluation by three radiologists and is according to the Bhalla score. Transp, transposition; ODA, outer dynein arm; SODA, shortened outer dynein arm.