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. Author manuscript; available in PMC: 2011 Jul 18.
Published in final edited form as: Genet Med. 2011 Jul;13(7):625–631. doi: 10.1097/GIM.0b013e3182142966

Table 4.

New onset cardiovascular abnormalities during the study period

Control ERT p-value
Echo Data
Ejection fraction <55% 3 (13%) 5 (10%) 0.70
ECG Data
Rhythm
 Sinus bradycardia 2 (7%) 3 (5%) 0.66
 Sinus tachycardia 0 (0%) 4 (7%) 0.30
Atrioventricular block 0 (0%) 0 (0%) --
Prolonged QRS duration 1 (4%) 2 (4%) 0.99
Prolonged QTc interval 3 (11%) 7 (13%) 0.99
Bundle Branch Block 1 (4%) 2 (4%) 0.99
Supraventricular Ectopy
 PAC 1 (4%) 1 (2%) 0.54
 SVT 0 (0%) 1 (2%) 0.99
Ventricular Ectopy
 PVC 0 (0%) 1 (2%) 0.99
 Ventricular Tachycardia 0 (0%) 0 (0%) --

ERT = enzyme replacement therapy, PAC = premature atrial contraction, SVT = supraventricular tachycardia, PVC = premature ventricular contraction. Percentages based on the number of patients who did not have the abnormality at baseline.