Table 3.
An affected individual with Peutz-Jeghers syndrome |
An affected individual with hereditary pancreatitis |
≥ 3 first-, second- or third-degree relatives with pancreatic cancer, with at least one pancreatic cancer in a first-degree relative |
A known mutation carrier of a BRCA1*, BRCA2, p16, MLH1*, MSH2*, MSH6*, or PMS2* mutation and at least one first- or second-degree relative with pancreatic cancer |
Screening may also be considered in individuals with 2 first-degree relatives with pancreatic cancer 80
Data are more limited in these categories