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. 2011 Aug 4;7(8):e1002214. doi: 10.1371/journal.pgen.1002214

Table 1. Summary of the motor phenotype quantification in the ALS matrix.

Conditions % Phenotype % Normal UAL N n Figure
Non Injected 2 94.8 99.2 753 32 n/a
Mis Fus AMO 6.9 81.6 N.D. 87 3 n/a
Sham Injected 3.5 87.7 N.D. 114 4 n/a
Fus AMO 56.9 25.9 75.9 437 12 2Ci + 3Bi + 5Aiv
Fus AMO + WT FUS 16.2 70.3 91.1 185 6 2Cii+3Bii
Fus AMO + R521H FUS 61.9 21.1 74.1 147 4 2Ciii
Fus AMO + R521C FUS 34.3 47.9 80.2 169 5 2Civ
Fus AMO + S57del FUS 19.1 63.8 92 94 3 2Cv
R521H FUS 38.4 42.6 78.3 284 9 2Cvi + 3Di + 5Ai
R521C FUS 18.5 63.1 93.1 157 5 2Cvii
S57del FUS 12.2 72.5 97.8 92 3 2Cviii
WT FUS 9.8 77.4 93.9 204 6 2Cix
Tardbp AMO 58.1 26.6 70.9 327 8 3Ai + 5Av
Tardbp AMO + WT TARDBP 19.9 58.9 86.1 151 4 3Aiii
WT TARDBP 18 61 89.1 128 3 n/a
Tardbp AMO + WT FUS 32.6 49.4 83.4 172 5 3Aii
Fus AMO + WT TARDBP 58.1 27.7 77.1 148 5 3Biii
Fus + Tardbp AMOs 59 20.9 69.3 139 4 5Avi
G348C TARDBP 54.3 23.5 75.6 221 6 3Ci + 5Aii
G348C TARDBP + R521H FUS 47.1 25 75.3 104 3 5Aiii
R521H FUS + WT TARDBP 30.8 40.7 78.1 91 3 3Diii
R521H FUS + WT FUS 35.6 41.4 78.9 87 3 3Dii
G348C TARDBP + WT TARDBP 44 21.1 70.5 109 3 3Ciii
G348C TARDBP + WT FUS 48.9 22.9 73 96 3 3Cii
WT SOD1 8 68.2 N.D. 88 3 n/a
Tardbp AMO + WT SOD1 58.5 25.5 71.8 94 3 3Aiv
Fus AMO + WT SOD1 57.1 29.5 76.2 112 3 3Biv
G348C TARDBP + WT SOD1 53.8 21.5 75.3 93 3 3Civ
R521H FUS + WT SOD1 38.8 41.2 75.9 85 3 3Div
Sod1 AMO 12.3 67.9 N.D. 81 3 n/a
Sod1 + Tardbp AMOs 55.8 25.2 71.9 104 3 3Av
Sod1 + Fus AMOs 58.7 25 75.4 92 2 3Bv
Sod1 AMO + G348C TARDBP 58.4 22.5 75.6 89 3 3Cv
Sod1 AMO + R521H FUS 39.2 40.2 78.2 102 3 3Dv
G93A SOD1 33.1 44.4 81.4 223 5 5Bi
G93A SOD1 + WT FUS 34.6 42.1 76.4 107 3 5Bii
G93A SOD1 + WT TARDBP 33 44 80.2 91 3 5Biii
G93A SOD1 + R521H FUS 58.8 17 67.9 153 5 5Biv
G93A SOD1 + G348C TARDBP 57.2 19.2 68.4 187 5 5Bv

Summary of the motor phenotype quantifications (TEER; % and UAL; µm) for all the conditions described in this study. After each experiment (n), embryos (N) were separated into four groups and the percentages were calculated for dead and developmentally deficient (2–20%, data not shown) as well as normally developed fish with delayed (phenotype) or normal swimming following the TEER. Also the length (µm) of the axonal projections (UAL) from motor neurons was assessed for each group. The last row indicates the Figure where these data are presented.