Table 3.

Primary Systemic Vasculitis Most Frequently Involving the CNS in Adults

SMALL-MEDIUM VESSEL VASCULITIS(*)

Wegener’s granulomatosis

Microscopic polyangiitis

Churg-Strauss syndrome

Cryoglobulinemic

vasculitis

Behçet’s disease

MEDIUM VESSEL VASCULITIS (**)

Polyarteritis nodosa

LARGE-VESSEL VASCULITIS

Giant-cell arteritis

Takayasu’s arteritis(***)

In children, Henoch-Shönlein purpura

^*and Kawasaki disease

^**may occasionally involve the CNS

^***Neurologic complications in Takayasu’s arteritis are mainly due to involvement of extacranial vessels.