TABLE 1.
CHARACTERISTICS OF PARTICIPANTS WITH CYSTIC FIBROSIS AT THE ENROLLMENT VISIT (N = 100)
| Characteristic | Mean (SD) or % |
|---|---|
| Age, mo | 14.0 (6.2) |
| Length | |
| cm | 74.1 (7.2) |
| Percentile | 32.7 (26.4) |
| Weight | |
| kg | 9.2 (2.0) |
| Percentile | 27.7 (26.3) |
| Male, % | 55 |
| Race, % | |
| White | 87 |
| Hispanic | 9 |
| African American | 2 |
| Asian or Pacific Islander | 1 |
| Other | 1 |
| Genotype, % | |
| ΔF508 homozygous | 55 |
| ΔF508 compound heterozygous | 37 |
| Other | 5 |
| Unknown/not done | 3 |
| Diagnosis suggested by newborn or prenatal screening, %* | 21 |
| Exposed to cigarette smoke, %† | 11 |
| Family history of asthma, %‡ | 30 |
| Pseudomonas isolated from respiratory culture, %§ | 12 |
| Shwachman score (41) | 69.9 (6.3) |
*
Newborn screening for CF was being performed at only two of the participating centers at the time of study enrollment: the University of Colorado and Children's Hospital Boston.
†
Defined as either mother smoked during pregnancy or child exposed to smoke after birth, by parent report.
‡
By parent report.
§
A total of 99 out of 100 participants were cultured at time of enrollment.