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Summary of the Literature and Our Cases
| Case No. | Mean Age, y | Sex | Site | Coexisting Lesions | Associated Syndromes |
|---|---|---|---|---|---|
| 30 (25 + 5*) | 41 (range, <1–80) | M:F 1.2:1 | Head, n = 4 Body and tail, n = 3 Diffuse, n = 17 |
Carcinoma, n = 3 Leiomyosarcoma, n = 1 |
Shwachman-Diamond syndrome, n = 3 Bannayan syndrome, n = 1 Johanson-Blizzard syndrome, n = 1 |
Our cases.
