Table 2.
Type of Angioedema | C1-INH level | C1-INH function | C4 | C3 | C1q |
Type I HAE | Low | Low | Low | Normal | Normal |
Type II HAE | Normal | Low | Low | Normal | Normal |
Type III HAE | Normal | Normal | Normal | Normal | Normal |
AAE | Low | Low | Low | Normal/Low | Low |
ACE inhibitor | Normal | Normal | Normal | Normal | Normal |
Idiopathic | Normal | Normal | Normal | Normal | Normal |
C1-INH: C1 inhibitor, HAE: hereditary angioedema, AAE: acquired angioedema, ACE: angiotensin-converting enzyme.