(A) Lipid accumulation assayed by Nile red staining in MEFs from
Parkin+/+ (WT) and
Parkin–/– (KO) after
BSA-conjugated oleate (0.5 and 1 mM) incubation. Values represent the fold
relative to BSA incubation and normalized to cell number. The values represent the
average of 5 independent experiments. (B) Parkin expression in HepG2
cells overexpressing vector, WT Parkin, and
∆Ubi-Parkin constructs. (C) Lipid
accumulation in HepG2 cells overexpressing vector, Parkin, and
∆Ubi-Parkin after oleate incubation (0.5 and 1
mM). (D) Relative fluorescence of Bodipy-labeled dodecanoic acid at
the end of 1,200-second incubation in HepG2 cells overexpressing Parkin compared
with vector controls. Values represent the fold relative to vector-transfected
HepG2 cells. (E) Lipid accumulation in SH-SY5Y neuroblastoma cells
overexpressing vector, Parkin, and ΔUbi-Parkin after 0.5 mM oleate
incubation. Values are normalized to protein concentration. (F) Lipid
accumulation in response to 0.25 and 0.5 mM oleate in transformed B cells from 3
patients with PARK2 mutations versus 4 WT control subjects.
Values were normalized to cell number. Data are displayed relative to control
cells exposed to BSA normalized to 1. Data are expressed as mean ± SD.
*P < 0.05; **P < 0.01 versus
control or vector.