Skip to main content
. 2011 Mar 11;184(2):172–179. doi: 10.1164/rccm.201010-1697CI

TABLE 3.

CONFIRMATORY DIAGNOSIS

Histopathologic Features
Immature lobular development
Decreased number of pulmonary capillaries located away from the alveolar epithelium
Thickened alveolar septae
Medial hypertrophy of small pulmonary arteries and muscularization of distal arterioles
Malposition of pulmonary vein branches adjacent to pulmonary arteries (same adventitial sheath)
Lymphangiectasis (30%)

Data from References 10, 13, 30.