A family with IGD + anosmia (Kallmann syndrome) demonstrating x-linked recessive inheritance and phenotypic features typical of KAL1. The proband, indicated by the arrow, has synkinesia in addition to his anosmic IGD, and carries a R191X mutation on the KAL1 gene on his X chromosome and a normal Y chromosome. His maternal uncle carries the same KAL1 mutation and has Kallmann syndrome with renal agenesis, and his maternal great-uncle with the mutation also has Kallmann syndrome. Typical of an x-linked recessive pedigree, no male-to-male transmission is seen and female carriers are asymptomatic.