Table 2.

Distribution of main clinical manifestations associated with fever episodes in different cohorts of patients with PFAPA

Author, year	N	Symptoms (%)
		Fever	Pharyngitis	Cervical adenopathy	Aphthous stomatitis	Headache	Abdominal pain
Marshall et al., 1987	12	100	75	67	75	NA	NA
Thomas et al., 1999	66	100	65	77	67	65	45
Padeh et al., 1999	28	100	100	100	68	18	18
Galanakis et al., 2002	15	100	100	87	33	NA	NA
Tasher et al., 2006	54	NA	96	61	39	46	65
Renko et al., 2007	35	100	29	21	21	NA	NA
Padeh et al., 2008	15	100	100	100	40	20	20
Pignataro et al., 2009	18	100	100	89	89	33	44
Gattorno et al., 2009	130	100	84	84	58	41	53
Garavello et al., 2009	39	100	97	85	59	NA	NA
Kovacs et al., 2010	14	100	93	86	21	NA	NA
De Cunto et al., 2010	12	100	100	83	67	NA	42
Brown et al., 2010	10	100	100	90	90	NA	40
Feder & Salazar, 2010	105	100	85	62	38	44	41
Dagan et al., 2010	57	100	NA	44	33	NA	35

NA: not available