Table 1.
Demographic Data of Subjects
| Subjects | Plasma Acylcarntitine Profiles (μmol/L) | ||||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| Post-prandially | Termination of fast | ||||||||||||
| Age (years) |
Gender | Height (cm) |
Weight (kg) |
BMI | Prior Symptoms | Free Carnitine |
C16:0 | C18:0 | C0/ (C16+C18) |
C16:0 | C18:0 | C0/ (C16+C18) |
|
| 1 | 4 | M | 109.0 | 20.3 | 24.0 | none | 44.8 | 0.026 | 0.021 | 307 | 0.059 | 0.025 | 156 |
| 2 | 3 | M | 92.0 | 16.6 | 19.6 | hypoglycemia & seizures with illness | 45.7 | 0.067 | 0.042 | 127 | 0.059 | 0.025 | 151 |
| 3 | 4 | M | 111.5 | 23.9 | 19.2 | none | 55.4 | 0.052 | 0.041 | 195 | 0.059 | 0.029 | 165 |
| 4 | 3 | M | 98.0 | 16.4 | 17.1 | none | 33.6 | 0.031 | 0.027 | 202 | 0.061 | 0.041 | 108 |
| 5 | 4 | F | 110.5 | 21.9 | 17.9 | lethargy with illness | 51.7 | 0.041 | 0.050 | 163 | 0.083 | 0.040 | 103 |
Individual subject data are presented. cm = centimeter; kg=kilograms; BMI=body mass index calculated as weight (kg)/ height (m2); prior symptoms = parental reports of symptoms prior to study enrollment; plasma acylcarnitine concentrations of free carnitine, C16:0 and C18:0 acylcarnitine and the C0/C16+C18 ratio one hour after a meal, and C16:0, C18:0, acylcarnitine and the C0/C16+C18 ratio at the time the fast was terminated. The fast was terminated at 18 hours of fasting for subjects 1, 3 and 4, at 16 hours of fasting for subject 2 and at 17 hours of fasting for subject 5.